Tests & Procedures Index



Treatment for Cystic Fibrosis

Treatment for cystic fibrosis (CF)

Specific treatment for CF will be determined by your child's doctor based on:

  • Your child's age, overall health, and medical history
  • Extent of the disease (body systems affected)
  • Expectations for the course of the disease
  • Your child's tolerance for specific medications, procedures, or therapies
  • Your opinion or preference

At the present time, there is no cure for CF. However, research in gene therapy is being performed. The gene that causes CF has been identified and there are hopes that this will lead to an increased understanding of the disease. Also being researched are different drug regimens to help stop CF. Goals of treatment are to ease severity of symptoms and slow the progress of the disease. Treatment may include:

  • Management of problems that cause lung obstruction, which may involve:
    • Chest physical therapy. This is to help loosen and clear lung secretions, which may include postural drainage, and devices, such as a percussor or flutter, which vibrate the chest wall and loosen secretions.
    • Exercise. This can help loosen mucus, stimulate coughing, and improve overall physical condition.
    • Medications, such as bronchodilators and anti-inflammatories. These are used to decrease inflammation, reduce mucus, draw water into the lungs to loosen mucus, and help breathing.
    • Antibiotics. These are used to treat infections.
  • Management of digestive problems, which may involve:
    • Appropriate diet
    • Pancreatic enzymes to aid digestion
    • Vitamin supplements
    • Treatments for intestinal obstructions
  • Psychosocial support. Provide help dealing with issues, such as independence, sterility, and sexuality, financial issues, and relationships.

Newer therapies include lung transplantation for patients with end-stage lung disease. The type of transplant done is usually a double lung transplant or a heart-lung transplant. Not everyone is a candidate for a lung transplant. Consult your child's doctor for more information.

With medical and psychosocial support, many children and adolescents with CF can cope well and lead a productive life.

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Online Resources of Respiratory Disorders

Last reviewed: 7/30/2012